[PMID]: | 29381971 |
[Au] Autor: | Yang X; Liu J; Ren Y; Richard SA; Zhang Y |
[Ad] Endereço: | Department of Neurosurgery, West China Hospital of Sichuan University, Chengdu, Sichuan, China. |
[Ti] Título: | Isolated intracranial Rosai-Dorfman disease mimicking petroclival meningioma in a child: Case report and review of the literature. |
[So] Source: | Medicine (Baltimore);96(47):e8754, 2017 Nov. |
[Is] ISSN: | 1536-5964 |
[Cp] País de publicação: | United States |
[La] Idioma: | eng |
[Ab] Resumo: | RATIONALE: Rosai -Dorfman disease (RDD) is a rare, idiopathic, and non-neoplastic histioproliferative disease with distinctive entity of unknown etiology. Central nervous system (CNS) RDD is uncommon, hence, isolated intracranial RDD is extremely rare. So far only 6 cases of CNS RDD with the lesions originating from petroclival region have been reported. We present a case of isolated intracranial RDD mimicking petroclival meningioma. PATIENT CONCERNS: A 14-year-old girl was admitted at our hospital with a 3-month history of dizziness, slowly progressing headache, and 2-month history of instability in walking. Cranial nerve deficits, including left facial paralysis, left facial numbness and left hearing loss, were evident on examination. DIAGNOSES: Initial diagnosis of petroclival meningioma was made according to preoperative magnetic resonance imaging. INTERVENTIONS: The lesion was resected subtotally and pathology confirmed RDD. The patient received gamma-knife treatment for the residual lesion. OUTCOMES: The patient recovered well and the residual lesion significantly retrogressed on follow-up images. LESSONS: Preoperative diagnosis of petroclival RDD is full of challenges. Although surgical resection of lesions is an effective treatment option, total resection is not highly recommended because the surgery-related defect must be minimal. Patient with residual lesion can be put on steroid therapy and/or radiotherapy, especially for IgG4 positive subset of RDD. |
[Mh] Termos MeSH primário: |
Encefalopatias/diagnóstico Histiocitose Sinusal/diagnóstico Neoplasias Meníngeas/diagnóstico Meningioma/diagnóstico
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[Mh] Termos MeSH secundário: |
Adolescente Diagnóstico Diferencial Feminino Seres Humanos Neoplasias da Base do Crânio/diagnóstico
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[Pt] Tipo de publicação: | CASE REPORTS; JOURNAL ARTICLE; REVIEW |
[Em] Mês de entrada: | 1802 |
[Cu] Atualização por classe: | 180208 |
[Lr] Data última revisão:
| 180208 |
[Sb] Subgrupo de revista: | AIM; IM |
[Da] Data de entrada para processamento: | 180201 |
[St] Status: | MEDLINE |
[do] DOI: | 10.1097/MD.0000000000008754 |
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